Fragile X Syndrome (SXF) is a genetic disorder that causes hereditary intellectual disability. Its prevalence is higher in men. In this article, a bibliographical review is presented to analyse, on the one hand, the degree of linguistic affectation and, on the other, the effectiveness of its evaluation or intervention. Based on certain inclusion and exclusion criteria, 19 articles were analysed, the results of which show a variability dependent on the instruments applied, with those based on guided language being especially effective. Therefore, favourable conclusions can be drawn when it comes to establishing evaluation or intervention programs in the future that meet the needs of the SXF population, with certain guarantees of success. Fragile X Syndrome (SXF) is a genetic disorder that causes hereditary intellectual disability. Its prevalence is higher in men. In this article, a bibliographical review is presented to analyse, on the one hand, the degree of linguistic affectation and, on the other, the effectiveness of its evaluation or intervention. Based on certain inclusion and exclusion criteria, 19 articles were analysed, the results of which show a variability dependent on the instruments applied, with those based on guided language being especially effective. Therefore, favourable conclusions can be drawn when it comes to establishing evaluation or intervention programs in the future that meet the needs of the SXF population, with certain guarantees of success.